{"id":26214,"date":"2024-06-25T12:07:43","date_gmt":"2024-06-25T19:07:43","guid":{"rendered":"https:\/\/ameripharmaspecialty.com\/?p=26214"},"modified":"2025-07-16T16:56:28","modified_gmt":"2025-07-16T23:56:28","slug":"exploring-seronegative-myasthenia-gravis-symptoms-subtypes-and-treatments","status":"publish","type":"post","link":"https:\/\/ameripharmaspecialty.com\/es\/myasthenia-gravis\/exploring-seronegative-myasthenia-gravis-symptoms-subtypes-and-treatments\/","title":{"rendered":"Explorando la miastenia gravis seronegativa: s\u00edntomas, subtipos y tratamientos"},"content":{"rendered":"<p>La miastenia gravis seronegativa (MGSn) es una afecci\u00f3n en la que la sangre del paciente carece de anticuerpos comunes detectables, como el receptor de acetilcolina (AChR) y el receptor de tirosina quinasa espec\u00edfico del m\u00fasculo (MuSK), que causan la miastenia gravis. La MG seronegativa es una forma poco frecuente de enfermedad rara y, a menudo, no se diagnostica.&nbsp;<\/p>\n\n\n\n<div  id=\"call-to-action-2626a4df632b30dc6cb6ad1654b758da\" style=\"\" class=\"ct_call_to_action\">\n\t<div class=\"container\">\n\t\t<div class=\"block-wrap cta\">\n\t\t\t<div class=\"block-column\">\n\t\t\t\t<div class=\"cta_headings\">\n\t\t\t\t\t\t\t\t\t\t\t<h4 class=\"cta__heading\">\n\t\t\t\t\t\t\tHable con un especialista sobre la asistencia con los copagos\t\t\t\t\t\t<\/h4>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\t<span class=\"cta_btn\">\n\t\t\t\t\t\t<a href=\"tel:8777780318\">(877) 778-0318<\/a>\n\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t<\/div>\n\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n\n<p>Generalmente, cuando a un paciente se le diagnostica MG, se detecta una cantidad detectable de anticuerpos AChR o anti-MuSK en la sangre. Sin embargo, en el caso de la SnMG, los pacientes no presentan anticuerpos AChR ni anti-MuSK en la sangre, pero aun as\u00ed presentan s\u00edntomas de MG, como p\u00e1rpados ca\u00eddos, visi\u00f3n borrosa y dificultad para respirar, tragar y hablar.&nbsp;<\/p>\n\n\n\n<p>De hecho, aproximadamente&nbsp;<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/15885043\/#:~:text=Around%2010%2D20%25%20of%20myasthenia,muscle%20specific%20kinase%20(MuSK).\">10-20%<\/a>&nbsp;De los pacientes con MG se diagnostican como seronegativos. Sin embargo, la cifra real podr\u00eda ser mayor, ya que es muy posible que muchos pacientes seronegativos con MG no hayan recibido un diagn\u00f3stico preciso.<\/p>\n\n\n\n<p>Este art\u00edculo analiza los aspectos b\u00e1sicos de la MG seronegativa, incluida la diferencia entre MG seronegativa y seropositiva, los subtipos, los s\u00edntomas, el diagn\u00f3stico y los tratamientos que se pueden considerar para la MG seronegativa.&nbsp;<\/p>\n\n\n\n<div id=\"ez-toc-container\" class=\"ez-toc-v2_0_82_2 counter-hierarchy ez-toc-counter ez-toc-custom ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Alternar tabla de contenido\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Palanca<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/ameripharmaspecialty.com\/es\/myasthenia-gravis\/exploring-seronegative-myasthenia-gravis-symptoms-subtypes-and-treatments\/#Difference_Between_Seronegative_and_Seropositive_Myasthenia_Gravis\" >Diferencia entre miastenia gravis seronegativa y seropositiva<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/ameripharmaspecialty.com\/es\/myasthenia-gravis\/exploring-seronegative-myasthenia-gravis-symptoms-subtypes-and-treatments\/#Subtypes_of_Seronegative_MG\" >Subtipos de MG seronegativa<\/a><ul class='ez-toc-list-level-3' ><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/ameripharmaspecialty.com\/es\/myasthenia-gravis\/exploring-seronegative-myasthenia-gravis-symptoms-subtypes-and-treatments\/#Double_Seronegative_MG\" >MG doble seronegativa<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/ameripharmaspecialty.com\/es\/myasthenia-gravis\/exploring-seronegative-myasthenia-gravis-symptoms-subtypes-and-treatments\/#Triple_Seronegative_MG\" >MG triple seronegativa<\/a><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/ameripharmaspecialty.com\/es\/myasthenia-gravis\/exploring-seronegative-myasthenia-gravis-symptoms-subtypes-and-treatments\/#What_Are_the_Symptoms_of_Seronegative_Myasthenia_Gravis_SnMG\" >\u00bfCu\u00e1les son los s\u00edntomas de la miastenia gravis seronegativa (SnMG)?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/ameripharmaspecialty.com\/es\/myasthenia-gravis\/exploring-seronegative-myasthenia-gravis-symptoms-subtypes-and-treatments\/#How_Is_Seronegative_Myasthenia_Gravis_SnMG_Diagnosed\" >\u00bfC\u00f3mo se diagnostica la miastenia gravis seronegativa (SnMG)?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-7\" href=\"https:\/\/ameripharmaspecialty.com\/es\/myasthenia-gravis\/exploring-seronegative-myasthenia-gravis-symptoms-subtypes-and-treatments\/#What_Are_the_Treatment_Options_for_Seronegative_Myasthenia_Gravis_SnMG\" >\u00bfCu\u00e1les son las opciones de tratamiento para la miastenia gravis seronegativa (SnMG)?<\/a><\/li><\/ul><\/nav><\/div>\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Difference_Between_Seronegative_and_Seropositive_Myasthenia_Gravis\"><\/span>Diferencia entre miastenia gravis seronegativa y seropositiva<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>El factor com\u00fan que los proveedores de atenci\u00f3n m\u00e9dica consideran para distinguir entre miastenia gravis seronegativa y seropositiva es verificar la presencia o ausencia de anticuerpos contra el receptor de acetilcolina (AChR) o el receptor de tirosina quinasa espec\u00edfico del m\u00fasculo (MuSK) en la sangre del paciente.<\/p>\n\n\n\n<p>Alrededor&nbsp;<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/15885043\/#:~:text=Around%2010%2D20%25%20of%20myasthenia,muscle%20specific%20kinase%20(MuSK).\">80-90%<\/a>&nbsp;de las personas diagnosticadas con MG tienen anticuerpos contra el receptor de acetilcolina (AChR) en la sangre. El primer anticuerpo detectado en pacientes con MG fue el receptor de acetilcolina (AChR).&nbsp;<\/p>\n\n\n\n<p>Anteriormente, cuando a los pacientes con MG no se les detectaban anticuerpos AChR, se dec\u00eda que ten\u00edan&nbsp;<a href=\"https:\/\/www.sciencedirect.com\/science\/article\/abs\/pii\/0022510X9190067H\">MG seronegativa<\/a>Sin embargo, con m\u00e1s investigaciones, se descubri\u00f3 que una prote\u00edna 4 relacionada con el receptor de lipoprote\u00edna de baja densidad (LRP4) est\u00e1 involucrada en la uni\u00f3n neuromuscular.&nbsp;&nbsp;<\/p>\n\n\n\n<p>En resumen, los pacientes&nbsp;<a href=\"https:\/\/www.ncbi.nlm.nih.gov\/pmc\/articles\/PMC7734299\/\">sin AChR o autoanticuerpos anti-MuSK en la sangre<\/a>&nbsp;son diagnosticados como MG seronegativos, mientras que aquellos con AChR o autoanticuerpos anti-MuSK son diagnosticados como MG seropositivos.&nbsp;<\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Subtypes_of_Seronegative_MG\"><\/span>Subtipos de MG seronegativa<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Diversas publicaciones han categorizado a\u00fan m\u00e1s la enfermedad MG seronegativa&nbsp;<a href=\"https:\/\/mghope.org\/different-types-of-mg\">en dos subtipos seg\u00fan la presencia o ausencia de anticuerpos<\/a>:<\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Double_Seronegative_MG\"><\/span>MG doble seronegativa<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>En la MG doble seronegativa, los anticuerpos AChR y MuSK est\u00e1n ausentes en la sangre del paciente.<\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Triple_Seronegative_MG\"><\/span>MG triple seronegativa<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>En la MG triple seronegativa, los anticuerpos AChR, MuSK y LRP4 est\u00e1n ausentes en la sangre del paciente.&nbsp;<\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"What_Are_the_Symptoms_of_Seronegative_Myasthenia_Gravis_SnMG\"><\/span>\u00bfCu\u00e1les son los s\u00edntomas de la miastenia gravis seronegativa (SnMG)?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"alignright size-full\"><img loading=\"lazy\" decoding=\"async\" width=\"420\" height=\"223\" src=\"https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/08\/droopy-eyelids.jpg\" alt=\"Seronegative myasthenia gravis patient with droopy eyelids\" class=\"wp-image-26427\" srcset=\"https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/08\/droopy-eyelids.jpg 420w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/08\/droopy-eyelids-300x159.jpg 300w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/08\/droopy-eyelids-86x46.jpg 86w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/08\/droopy-eyelids-167x89.jpg 167w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/08\/droopy-eyelids-280x149.jpg 280w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/08\/droopy-eyelids-370x196.jpg 370w\" sizes=\"auto, (max-width: 420px) 100vw, 420px\" \/><\/figure>\n<\/div>\n\n\n<p>Los s\u00edntomas de la SnMG son los mismos que los de la MG seropositiva. Al igual que la MG seropositiva, la MG seronegativa puede ser ocular o generalizada. Sin embargo,&nbsp;<a href=\"https:\/\/www.jkna.org\/journal\/view.php?number=3939\">La incidencia de MG ocular es mayor en pacientes con MG seronegativos<\/a>&nbsp;que en pacientes seropositivos con MG, y los s\u00edntomas pueden variar de leves a graves. Los s\u00edntomas comunes incluyen:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>p\u00e1rpados ca\u00eddos<\/li>\n\n\n\n<li>Visi\u00f3n borrosa o doble<\/li>\n\n\n\n<li>Dificultad para masticar, tragar y hablar.<\/li>\n\n\n\n<li>debilidad de los m\u00fasculos faciales<\/li>\n\n\n\n<li>Dificultad para respirar (en casos graves)<\/li>\n<\/ul>\n\n\n\n<p>Los s\u00edntomas empeoran con la actividad repetitiva y mejoran con el descanso.&nbsp;<\/p>\n\n\n\n<div  id=\"call-to-action-fe5650a0ed273696ad7b68504272f13e\" style=\"\" class=\"ct_call_to_action\">\n\t<div class=\"container\">\n\t\t<div class=\"block-wrap cta\">\n\t\t\t<div class=\"block-column\">\n\t\t\t\t<div class=\"cta_headings\">\n\t\t\t\t\t\t\t\t\t\t\t<h4 class=\"cta__heading\">\n\t\t\t\t\t\t\t\u00bfPuede ayudar la IgIV? | Informaci\u00f3n gratuita sobre el tratamiento con IgIV | \u00bfEs dif\u00edcil diagnosticarla?\t\t\t\t\t\t<\/h4>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\t<span class=\"cta_btn\">\n\t\t\t\t\t\t<a href=\"#form\">Programar una consulta<\/a>\n\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t<\/div>\n\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"How_Is_Seronegative_Myasthenia_Gravis_SnMG_Diagnosed\"><\/span>\u00bfC\u00f3mo se diagnostica la miastenia gravis seronegativa (SnMG)?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>El diagn\u00f3stico de pacientes con MG seronegativos requiere un conjunto de habilidades diagn\u00f3sticas avanzadas en comparaci\u00f3n con los pacientes con MG seropositivos.<\/p>\n\n\n\n<p>Por lo general, un m\u00e9dico especializado en miastenia gravis realiza una revisi\u00f3n exhaustiva de la historia cl\u00ednica del paciente y la gravedad de los s\u00edntomas y realiza una prueba de detecci\u00f3n que incluye:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>An\u00e1lisis de sangre para comprobar la presencia o ausencia de autoanticuerpos AChr, MuSK y LRP4<\/li>\n\n\n\n<li>Electromiograf\u00eda (EMG)<\/li>\n\n\n\n<li>Estimulaci\u00f3n nerviosa repetitiva (ERN)<\/li>\n\n\n\n<li>Electromiograf\u00eda de fibra \u00fanica (SFEMG)<\/li>\n<\/ul>\n\n\n\n<p>Recientemente, se ha descubierto que una nueva t\u00e9cnica llamada prueba de ensayo basado en c\u00e9lulas (CBA) es beneficiosa para diagnosticar pacientes seronegativos.&nbsp;<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/35366559\/\">estudiar<\/a>&nbsp;Un estudio publicado en la Revista de Neuroinmunolog\u00eda inform\u00f3 que, tras la evaluaci\u00f3n de 99 pacientes seronegativos con MG mediante un ensayo celular (CBA), 18 pacientes dieron positivo en AChR. Estos hallazgos respaldan el uso del CBA de AChR agrupado para el diagn\u00f3stico de MG seronegativa.&nbsp;<\/p>\n\n\n\n<p>De manera similar, otro&nbsp;<a href=\"https:\/\/jnnp.bmj.com\/content\/93\/9\/995.abstract\">estudiar<\/a>&nbsp;informaron los mismos resultados y destacaron la utilidad diagn\u00f3stica de realizar ACB en pacientes con MG seronegativos.&nbsp;<\/p>\n\n\n\n<p>En la mayor\u00eda de los casos, los pacientes que dan negativo en las pruebas de MG suelen ser pasados por alto por los profesionales m\u00e9dicos, lo que los pone en riesgo de recibir una atenci\u00f3n deficiente que se brinda con demasiada lentitud.&nbsp;<\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"What_Are_the_Treatment_Options_for_Seronegative_Myasthenia_Gravis_SnMG\"><\/span>\u00bfCu\u00e1les son las opciones de tratamiento para la miastenia gravis seronegativa (SnMG)?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Los pacientes con MG seronegativa suelen tener dificultades para recibir tratamiento. Incluso si lo reciben, es posible que no reciban la atenci\u00f3n necesaria para optimizar sus s\u00edntomas. Dado que la MG seronegativa es dif\u00edcil de diagnosticar, su tratamiento puede llevar m\u00e1s tiempo que el de otras afecciones.&nbsp;<\/p>\n\n\n\n<p>Actualmente, la mayor\u00eda de los nuevos tratamientos aprobados por la FDA en el mercado son solo para pacientes con miastenia gravis seropositiva. Sin embargo, los pacientes con miastenia gravis seronegativa pueden probar las siguientes opciones de tratamiento bajo la supervisi\u00f3n de sus profesionales de la salud:&nbsp;<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Medicamentos (por ejemplo, Mestinon)<\/li>\n\n\n\n<li>Corticosteroides (por ejemplo, prednisona, etc.)<\/li>\n\n\n\n<li><a href=\"https:\/\/ameripharmaspecialty.com\/es\/ivig\/ivig\/\/ivig\/\">Inmunoglobulina intravenosa (IVIG)<\/a>&nbsp;o&nbsp;<a href=\"https:\/\/ameripharmaspecialty.com\/es\/ivig\/what-is-scig\/\">inmunoglobulina subcut\u00e1nea (SCIG)<\/a>)<\/li>\n\n\n\n<li>Plasmaf\u00e9resis (PLEX)<\/li>\n\n\n\n<li>Terapia inmunosupresora<\/li>\n\n\n\n<li><a href=\"https:\/\/ameripharmaspecialty.com\/es\/myasthenia-gravis\/thymectomy-for-myasthenia-gravis-what-patients-need-to-know\/\">Timectom\u00eda<\/a><\/li>\n<\/ul>\n\n\n\n<p>Se est\u00e1n realizando investigaciones sobre la miastenia gravis seronegativa (MGSn). Los investigadores a\u00fan intentan comprender qu\u00e9 tipos de anticuerpos o prote\u00ednas intervienen en esta forma de MG para poder desarrollar diagn\u00f3sticos y planes de tratamiento precisos para los pacientes.&nbsp;<\/p>","protected":false},"excerpt":{"rendered":"<p>La miastenia gravis seronegativa (SnMG) es una afecci\u00f3n en la que la sangre de un paciente no tiene anticuerpos comunes detectables, como el receptor de acetilcolina (AChR) y el receptor de tirosina quinasa espec\u00edfico del m\u00fasculo (MuSK), que causan miastenia gravis.<\/p>","protected":false},"author":7,"featured_media":26215,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":true,"om_disable_all_campaigns":false,"_uag_custom_page_level_css":"","footnotes":""},"categories":[10],"tags":[8],"class_list":["post-26214","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-myasthenia-gravis","tag-dr-christine-leduc"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.4 - 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Sus \u00e1reas de especializaci\u00f3n son la atenci\u00f3n al cliente y el conocimiento de medicamentos especializados. Tras haber trabajado en el sector servicios, ha adquirido las habilidades de atenci\u00f3n al cliente necesarias para comprender las necesidades de sus pacientes. Actualmente, la Dra. Leduc imparte clases a estudiantes de la Universidad Marshall B. Ketchum, la Universidad de Kansas y la Universidad Midwestern. En su tiempo libre, disfruta de viajar, la reposter\u00eda y la jardiner\u00eda. 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