{"id":24873,"date":"2024-02-12T09:35:13","date_gmt":"2024-02-12T09:35:13","guid":{"rendered":"https:\/\/ameripharmaspecialty.com\/?p=24873"},"modified":"2025-01-28T14:59:46","modified_gmt":"2025-01-28T21:59:46","slug":"understanding-lambert-eaton-syndrome-a-rare-disorder","status":"publish","type":"post","link":"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/understanding-lambert-eaton-syndrome-a-rare-disorder\/","title":{"rendered":"Comprender el s\u00edndrome de Lambert-Eaton: un trastorno poco com\u00fan"},"content":{"rendered":"<p>El s\u00edndrome de Lambert-Eaton (SMLE) es un trastorno poco com\u00fan que se produce como resultado de un ataque del sistema inmunitario a la uni\u00f3n neuromuscular (el punto donde los nervios env\u00edan se\u00f1ales a los m\u00fasculos). El da\u00f1o en la uni\u00f3n neuromuscular provoca una transmisi\u00f3n deficiente de las se\u00f1ales nerviosas a los m\u00fasculos, lo que provoca debilidad muscular gradual y una serie de otros s\u00edntomas.&nbsp;<\/p>\n\n\n\n<div  id=\"call-to-action-bf75fa766f4e2880279842f71c40f063\" style=\"\" class=\"ct_call_to_action\">\n\t<div class=\"container\">\n\t\t<div class=\"block-wrap cta\">\n\t\t\t<div class=\"block-column\">\n\t\t\t\t<div class=\"cta_headings\">\n\t\t\t\t\t\t\t\t\t\t\t<h4 class=\"cta__heading\">\n\t\t\t\t\t\t\tHabla con un especialista\t\t\t\t\t\t<\/h4>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"cta__sub__heading\">\n\t\t\t\t\t\t\tAcerca de la asistencia para copagos\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\t<span class=\"cta_btn\">\n\t\t\t\t\t\t<a href=\"tel:8777780318\">(877) 778-0318<\/a>\n\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t<\/div>\n\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n\n<p>Esta condici\u00f3n a menudo se denomina s\u00edndrome miast\u00e9nico de Lambert-Eaton debido a las similitudes de sus s\u00edntomas con&nbsp;<a href=\"https:\/\/ameripharmaspecialty.com\/es\/myasthenia-gravis\/myasthenia-gravis\/\">miastenia gravis<\/a>&nbsp;(un tipo de trastorno de la uni\u00f3n neuromuscular).<\/p>\n\n\n\n<p>La prevalencia del s\u00edndrome de Lambert-Eaton es 46 veces menor que la de la miastenia gravis y afecta principalmente a hombres que a mujeres.<\/p>\n\n\n\n<p>Por lo tanto, si a usted o a un ser querido le han diagnosticado recientemente LEMS, es importante que comprenda esta afecci\u00f3n neurol\u00f3gica para poder controlarla adecuadamente.&nbsp;<\/p>\n\n\n\n<p>Este art\u00edculo proporciona una comprensi\u00f3n b\u00e1sica del LEMS, incluida su causa subyacente, los signos y s\u00edntomas comunes y varias estrategias de tratamiento para ayudarlo a controlar esta afecci\u00f3n.<\/p>\n\n\n\n<div id=\"ez-toc-container\" class=\"ez-toc-v2_0_82_2 counter-hierarchy ez-toc-counter ez-toc-custom ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Alternar tabla de contenido\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Palanca<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/understanding-lambert-eaton-syndrome-a-rare-disorder\/#Basics_of_Lambert-Eaton_Syndrome\" >Conceptos b\u00e1sicos del s\u00edndrome de Lambert-Eaton<\/a><ul class='ez-toc-list-level-3' ><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/understanding-lambert-eaton-syndrome-a-rare-disorder\/#Underlying_Cause_of_LEMS\" >Causa subyacente del LEMS<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/understanding-lambert-eaton-syndrome-a-rare-disorder\/#Common_Signs_and_Symptoms_of_LEMS\" >Signos y s\u00edntomas comunes del LEMS<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/understanding-lambert-eaton-syndrome-a-rare-disorder\/#Diagnosis_and_Tests_for_LEMS\" >Diagn\u00f3stico y pruebas para el LEMS<\/a><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/understanding-lambert-eaton-syndrome-a-rare-disorder\/#Treatment_Options_for_Lambert-Eaton_Syndrome\" >Opciones de tratamiento para el s\u00edndrome de Lambert-Eaton<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/understanding-lambert-eaton-syndrome-a-rare-disorder\/#Prognosis_of_Lambert-Eaton_Syndrome\" >Pron\u00f3stico del s\u00edndrome de Lambert-Eaton<\/a><\/li><\/ul><\/nav><\/div>\n<h2 class=\"wp-block-heading\" id=\"h-basics-of-lambert-eaton-syndrome\"><span class=\"ez-toc-section\" id=\"Basics_of_Lambert-Eaton_Syndrome\"><\/span>Conceptos b\u00e1sicos del s\u00edndrome de Lambert-Eaton<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Imagina que quieres realizar una actividad que requiere la funci\u00f3n muscular. Tu sistema nervioso (cerebro) env\u00eda se\u00f1ales a trav\u00e9s de los nervios a tus m\u00fasculos para realizar esa acci\u00f3n. Estos nervios liberan una sustancia qu\u00edmica llamada&nbsp;<a href=\"https:\/\/my.clevelandclinic.org\/health\/articles\/24568-acetylcholine-ach\">acetilcolina<\/a>, que indica a las fibras musculares que se contraigan. La liberaci\u00f3n de acetilcolina se facilita principalmente por los canales de calcio dependientes de voltaje presentes en los extremos de las terminaciones nerviosas. Por lo tanto, cuando estos canales se activan durante la transmisi\u00f3n de se\u00f1ales nerviosas, estimulan la liberaci\u00f3n de acetilcolina, que se une a sus receptores en la fibra muscular y provoca la contracci\u00f3n muscular.<\/p>\n\n\n\n<p>Sin embargo, en las personas con s\u00edndrome de Lambert-Eaton, el sistema inmunitario produce autoanticuerpos que bloquean los canales de calcio en las terminaciones nerviosas. Este bloqueo provoca una menor liberaci\u00f3n de acetilcolina, insuficiente para la contracci\u00f3n muscular normal, y como resultado, las personas con LEMS experimentan debilidad muscular y fatiga.<\/p>\n\n\n\n<p>La enfermedad recibe su nombre de Edward Lambert y Lee Eaton, dos neur\u00f3logos que describieron por primera vez los s\u00edntomas del s\u00edndrome miast\u00e9nico en la d\u00e9cada de 1950.<\/p>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-underlying-cause-of-lems\"><span class=\"ez-toc-section\" id=\"Underlying_Cause_of_LEMS\"><\/span>Causa subyacente del LEMS<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Los investigadores creen que el sistema inmunitario es el factor determinante de la aparici\u00f3n del LEMS. Adem\u00e1s, en el 50% al 60% de los casos, esta enfermedad tambi\u00e9n est\u00e1 altamente asociada.&nbsp;<a href=\"https:\/\/www.mda.org\/disease\/lambert-eaton-myasthenic-syndrome\">con ciertos tipos de c\u00e1ncer, en particular el c\u00e1ncer de pulm\u00f3n de c\u00e9lulas peque\u00f1as (CPCP)<\/a>.&nbsp;&nbsp;&nbsp;<\/p>\n\n\n\n<p>Se teoriza que cuando el sistema inmunitario combate las c\u00e9lulas cancerosas, tambi\u00e9n ataca por error las terminaciones nerviosas, ya que estas contienen algunas de las mismas prote\u00ednas presentes en ellas. Esta confusi\u00f3n se denomina \u00abs\u00edndrome paraneopl\u00e1sico\u00bb, que puede manifestarse como LEMS.<\/p>\n\n\n\n<p>Sin embargo, no todos los c\u00e1nceres causan LEMS. Actualmente se desconoce el desencadenante del LEMS sin c\u00e1ncer; sin embargo, se teoriza que genes vinculados a la autoinmunidad podr\u00edan ser la causa. Las personas diagnosticadas con LEMS sin c\u00e1ncer tambi\u00e9n son mucho m\u00e1s j\u00f3venes, con una edad promedio de inicio de 35 a\u00f1os.&nbsp;&nbsp;<\/p>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-common-signs-and-symptoms-of-lems\"><span class=\"ez-toc-section\" id=\"Common_Signs_and_Symptoms_of_LEMS\"><\/span>Signos y s\u00edntomas comunes del LEMS<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<div  id=\"image-with-text-05be45a20e2280c9fecc01a0a7ff6e91\" style=\"\" class=\"ct_image_with_text\">\n        <div class=\"container\">\n        <div class=\"block-spacing block-wrap image_with_text\">\n                            <div class=\"image_with_text_content\">\n                    <p>La aparici\u00f3n de los s\u00edntomas del LEMS es gradual y suele desarrollarse en semanas o meses. Sin embargo, en pacientes con c\u00e1ncer de pulm\u00f3n de c\u00e9lulas peque\u00f1as, la progresi\u00f3n de los s\u00edntomas del LEMS podr\u00eda ser r\u00e1pida.<\/p>\n<p>El s\u00edntoma com\u00fan del LEMS es la debilidad muscular proximal, y la distribuci\u00f3n de la debilidad muscular comienza en las extremidades inferiores (parte superior de las piernas y caderas) y se desplaza hacia arriba hasta los m\u00fasculos del hombro.<\/p>\n                <\/div>\n                                        <div class=\"image_with_text_media\">\n                    <picture>\n                                                <source loading=\"lazy\" media=\"(min-width:768px)\" srcset=\"https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/man-shoulder.jpg\">\n                        <img decoding=\"async\" loading=\"lazy\" src=\"https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/man-shoulder.jpg\" alt=\"https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/man-shoulder.jpg\" style=\"width:auto;\">\n                    <\/picture>\n                <\/div>\n                    <\/div>\n    <\/div>\n<\/div>\n\n\n<p>Las personas con LEMS pueden experimentar dificultad para caminar, subir escaleras y levantarse de sillas debido a la debilidad muscular de la cadera. Con el tiempo, la debilidad muscular mejora temporalmente tras la actividad muscular repetitiva, lo cual es una caracter\u00edstica \u00fanica de esta afecci\u00f3n.<\/p>\n\n\n\n<p>Otros s\u00edntomas del LEMS incluyen:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Sensaci\u00f3n de hormigueo en las manos o los pies.<\/li>\n\n\n\n<li>Rigidez y dolor muscular<\/li>\n\n\n\n<li>Fatiga<\/li>\n\n\n\n<li>Dificultad para caminar<\/li>\n\n\n\n<li>Debilidad oculobulbar, observada en aproximadamente el 701% de los pacientes. La debilidad ocular incluye ptosis y diplop\u00eda.<\/li>\n\n\n\n<li>Disfagia (dificultad para tragar)<\/li>\n\n\n\n<li><a href=\"https:\/\/www.mayoclinic.org\/diseases-conditions\/dysarthria\/symptoms-causes\/syc-20371994\">Disartria<\/a>&nbsp;(dificultad para hablar)<\/li>\n\n\n\n<li>Insuficiencia respiratoria (poco frecuente, pero puede ocurrir en la etapa avanzada del LEMS)<\/li>\n<\/ul>\n\n\n\n<p>La disfunci\u00f3n auton\u00f3mica tambi\u00e9n es una preocupaci\u00f3n frecuente en el LEMS y se observa en aproximadamente entre el 80 y el 96 % de los pacientes. Los s\u00edntomas m\u00e1s frecuentes son sequedad bucal, estre\u00f1imiento y disfunci\u00f3n er\u00e9ctil.<\/p>\n\n\n\n<div  id=\"call-to-action-55f59b83403dfd57d4f3b440d48f96fe\" style=\"\" class=\"ct_call_to_action\">\n\t<div class=\"container\">\n\t\t<div class=\"block-wrap cta\">\n\t\t\t<div class=\"block-column\">\n\t\t\t\t<div class=\"cta_headings\">\n\t\t\t\t\t\t\t\t\t\t\t<h4 class=\"cta__heading\">\n\t\t\t\t\t\t\t\u00bfPuede ayudar la IgIV?\t\t\t\t\t\t<\/h4>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"cta__sub__heading\">\n\t\t\t\t\t\t\tInformaci\u00f3n gratuita sobre el tratamiento con IgIV\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\t<span class=\"cta_btn\">\n\t\t\t\t\t\t<a href=\"#form\">Consulte a un especialista en IgIV<\/a>\n\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t<\/div>\n\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-diagnosis-and-tests-for-lems\"><span class=\"ez-toc-section\" id=\"Diagnosis_and_Tests_for_LEMS\"><\/span>Diagn\u00f3stico y pruebas para el LEMS<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Los neur\u00f3logos realizan una combinaci\u00f3n de pruebas, incluyendo una evaluaci\u00f3n f\u00edsica. El neur\u00f3logo tambi\u00e9n considerar\u00e1 el historial m\u00e9dico y de medicaci\u00f3n del paciente y observar\u00e1 los s\u00edntomas. Otras pruebas m\u00e9dicas incluyen:&nbsp;<\/p>\n\n\n\n<p><strong>An\u00e1lisis de sangre<\/strong><\/p>\n\n\n\n<p>Esta prueba verifica la presencia de&nbsp;<a href=\"https:\/\/www.jnj.com\/innovation\/what-are-autoantibodies\">autoanticuerpos<\/a>&nbsp;En el sistema circulatorio del paciente. Aproximadamente entre el 85% y el 95% de las personas con LEMS presentan estos autoanticuerpos en la sangre.&nbsp;<\/p>\n\n\n\n<p><strong>Electromiograf\u00eda<\/strong><\/p>\n\n\n\n<p>Esta prueba verifica c\u00f3mo est\u00e1n funcionando sus nervios y m\u00fasculos.<\/p>\n\n\n\n<p><strong>Tomograf\u00eda computarizada (TC), resonancia magn\u00e9tica (RM) o rayos X<\/strong><\/p>\n\n\n\n<p>Las tomograf\u00edas computarizadas, las resonancias magn\u00e9ticas y las radiograf\u00edas se utilizan para comprobar neoplasias malignas subyacentes, como la presencia de c\u00e1ncer de pulm\u00f3n de c\u00e9lulas peque\u00f1as (CPCP).<\/p>\n\n\n\n<p>En algunos casos, el LEMS puede aparecer de 2 a 3 a\u00f1os antes que el c\u00e1ncer, y si a una persona se le diagnostica LEMS, los proveedores de atenci\u00f3n m\u00e9dica recomiendan ex\u00e1menes de detecci\u00f3n de c\u00e1ncer cada 3 a 6 meses durante al menos 2 a\u00f1os.&nbsp;<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-treatment-options-for-lambert-eaton-syndrome\"><span class=\"ez-toc-section\" id=\"Treatment_Options_for_Lambert-Eaton_Syndrome\"><\/span>Opciones de tratamiento para el s\u00edndrome de Lambert-Eaton<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Aunque no existe una cura conocida para el LEMS, ciertos medicamentos y enfoques terap\u00e9uticos pueden ayudar a los pacientes a controlar sus s\u00edntomas. El objetivo principal del tratamiento es tratar la causa subyacente, como el c\u00e1ncer, y controlar los s\u00edntomas del LEMS. Por lo tanto, si tiene LEMS asociado a un c\u00e1ncer como el CPCP, tratar primero la causa subyacente (el c\u00e1ncer) puede ayudar a tratar el LEMS.&nbsp;<\/p>\n\n\n\n<p>Los proveedores de atenci\u00f3n m\u00e9dica recomiendan una combinaci\u00f3n de cirug\u00eda, quimioterapia y radioterapia seg\u00fan el tipo de c\u00e1ncer que tenga el paciente.&nbsp;<\/p>\n\n\n\n<p>En el caso del tratamiento del LEMS, generalmente se utilizan medicamentos dise\u00f1ados para reducir los s\u00edntomas del LEMS y terapias inmunomoduladoras que suprimen la respuesta inmunitaria\/ataque inmunol\u00f3gico a los nervios.&nbsp;<\/p>\n\n\n\n<p>Los medicamentos m\u00e1s eficaces que se recomiendan como tratamiento de primera l\u00ednea para reducir los s\u00edntomas del LEMS incluyen:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>Amifampridina (<a href=\"https:\/\/firdapsehcp.com\/?utm_source=google&amp;utm_medium=cpc&amp;utm_campaign=22_Firdapse_HCP_Branded_Brand&amp;utm_content=&amp;utm_term=firdapse&amp;gad_source=1&amp;gclid=CjwKCAiA44OtBhAOEiwAj4gpOaXLXE9Y3qJOCDRSsWxdIucn3M_4RkIEV8TGGfGqqcRXaOlZPa3ZLhoC1vEQAvD_BwE&amp;gclsrc=aw.ds\">Firdapse<\/a>):<\/strong>Este medicamento aumenta la liberaci\u00f3n de acetilcolina y, por lo tanto, mejora la transmisi\u00f3n de se\u00f1ales a los m\u00fasculos. La dosis inicial recomendada de Firdapse para adultos es de 15 a 30 mg al d\u00eda, dividida en tres o cuatro dosis. Su profesional de la salud puede aumentar la dosis hasta un m\u00e1ximo de 80 mg al d\u00eda.<\/li>\n\n\n\n<li><strong>Guanidina:<\/strong>&nbsp;Este medicamento tambi\u00e9n aumenta la liberaci\u00f3n de acetilcolina y mejora las contracciones musculares. La dosis inicial recomendada de guanidina es de 15 a 30 mg\/kg\/d\u00eda, dividida en tres o cuatro dosis. La dosis puede aumentarse seg\u00fan la tolerabilidad hasta un m\u00e1ximo de 35 mg\/kg\/d\u00eda.<\/li>\n\n\n\n<li><strong>Piridostigmina (<a href=\"https:\/\/www.webmd.com\/drugs\/2\/drug-3740\/mestinon-oral\/details\">Mestin\u00f3n<\/a>):<\/strong>&nbsp;Este medicamento act\u00faa previniendo la degradaci\u00f3n de la acetilcolina en la uni\u00f3n entre los nervios y los m\u00fasculos. Al aumentar la cantidad de acetilcolina disponible, puede ayudar a aumentar la fuerza muscular. El uso de Mestinon para esta indicaci\u00f3n se considera fuera de indicaci\u00f3n, lo que significa que no est\u00e1 aprobado por la FDA para este uso. La dosis de Mestinon para el LEMS var\u00eda, ya que el rango es amplio y se basa en la tolerabilidad. Su profesional de la salud le recetar\u00e1 la dosis adecuada.&nbsp;<\/li>\n<\/ul>\n\n\n\n<p>A veces, cuando la medicaci\u00f3n no funciona bien y el paciente persiste con una debilidad persistente, los profesionales de la salud recomiendan terapias inmunomoduladoras o inmunosupresoras que suprimen la respuesta inmunitaria hiperactiva. Estas terapias incluyen:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li><a href=\"https:\/\/ameripharmaspecialty.com\/es\/ivig\/ivig\/\/ivig\/\"><strong>Terapia con inmunoglobulina (IVIG)<\/strong><\/a>, un procedimiento en el que se inyectan anticuerpos en el cuerpo que impiden temporalmente que el sistema inmunitario ataque los nervios.<\/li>\n\n\n\n<li><a href=\"https:\/\/ameripharmaspecialty.com\/es\/ivig\/ivig-vs-plasmapheresis\/\"><strong>Plasmaf\u00e9resis<\/strong><\/a>, un procedimiento para filtrar los autoanticuerpos del cuerpo, previniendo as\u00ed el da\u00f1o a los nervios.&nbsp;&nbsp;<\/li>\n\n\n\n<li><strong>Medicamentos inmunosupresores&nbsp;<\/strong>para reducir la actividad de su sistema inmunol\u00f3gico.&nbsp;<\/li>\n<\/ul>\n\n\n\n<p>Adem\u00e1s de los medicamentos y las terapias inmunosupresoras, un estilo de vida saludable puede ayudar a prevenir la aparici\u00f3n del LEMS. Dado que, en el 50% de los casos, la aparici\u00f3n del LEMS se asocia con c\u00e1ncer de pulm\u00f3n, evitar el tabaco puede ayudar a prevenir el c\u00e1ncer.&nbsp;<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-prognosis-of-lambert-eaton-syndrome\"><span class=\"ez-toc-section\" id=\"Prognosis_of_Lambert-Eaton_Syndrome\"><\/span>Pron\u00f3stico del s\u00edndrome de Lambert-Eaton<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Siempre que la afecci\u00f3n subyacente se trate con prontitud, el pron\u00f3stico del LEMS es favorable. Los tratamientos y f\u00e1rmacos inmunosupresores generalmente tuvieron un efecto positivo en los pacientes con LEMS, aumentando sus probabilidades de supervivencia y mejorando su calidad de vida.&nbsp;<\/p>\n\n\n\n<p>Despu\u00e9s del diagn\u00f3stico,&nbsp;<a href=\"https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK507891\/\">85% de los pacientes recuperan la independencia en las actividades diarias<\/a>&nbsp;dentro de un a\u00f1o de tratamiento.&nbsp;<\/p>","protected":false},"excerpt":{"rendered":"<p>El s\u00edndrome de Lambert-Eaton (SMLE) es un trastorno poco com\u00fan que se produce como resultado de un ataque del sistema inmunitario a la uni\u00f3n neuromuscular (el punto donde los nervios env\u00edan se\u00f1ales a los m\u00fasculos). El da\u00f1o en la uni\u00f3n neuromuscular provoca una transmisi\u00f3n deficiente de las se\u00f1ales nerviosas a los m\u00fasculos, lo que provoca debilidad muscular gradual y una serie de otros s\u00edntomas.<\/p>","protected":false},"author":27,"featured_media":24875,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":true,"om_disable_all_campaigns":false,"_uag_custom_page_level_css":"","footnotes":""},"categories":[4],"tags":[],"class_list":["post-24873","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-other-health-conditions"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.5 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Understanding Lambert-Eaton Syndrome: A Rare Disorder - AmeriPharma\u00ae Specialty Care<\/title>\n<meta name=\"description\" content=\"Learn about the basics of Lambert-Eaton syndrome. 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Samantha Kaeberlein, PharmD","image":{"@type":"ImageObject","inLanguage":"es","@id":"https:\/\/secure.gravatar.com\/avatar\/fabe5720eac93901a4790d5e25493a8cf2fdf076c21466237b10de4cc181b9d2?s=96&d=mm&r=g","url":"https:\/\/secure.gravatar.com\/avatar\/fabe5720eac93901a4790d5e25493a8cf2fdf076c21466237b10de4cc181b9d2?s=96&d=mm&r=g","contentUrl":"https:\/\/secure.gravatar.com\/avatar\/fabe5720eac93901a4790d5e25493a8cf2fdf076c21466237b10de4cc181b9d2?s=96&d=mm&r=g","caption":"Dr. Samantha Kaeberlein, PharmD"},"description":"La Dra. Samantha Kaeberlein, PharmD, naci\u00f3 y creci\u00f3 en Canton, Ohio. Obtuvo su t\u00edtulo en farmacia en la Universidad M\u00e9dica del Noreste de Ohio (NEOMED) en 2020. Lo m\u00e1s gratificante de su trabajo es brindar orientaci\u00f3n m\u00e9dica para que los pacientes puedan tomar decisiones informadas y completas sobre su atenci\u00f3n m\u00e9dica. Sus \u00e1reas de especializaci\u00f3n son la geriatr\u00eda y los cuidados a largo plazo. En su tiempo libre, disfruta de pasar tiempo al aire libre, leer y encontrar el mejor caf\u00e9 de Estados Unidos.","url":"https:\/\/ameripharmaspecialty.com\/es\/author\/samantha\/"}]}},"uagb_featured_image_src":{"full":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction.jpg",1280,853,false],"thumbnail":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-150x150.jpg",150,150,true],"medium":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-300x200.jpg",300,200,true],"medium_large":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-768x512.jpg",768,512,true],"large":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-1024x682.jpg",1024,682,true],"1536x1536":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction.jpg",1280,853,false],"2048x2048":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction.jpg",1280,853,false],"trp-custom-language-flag":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction.jpg",18,12,false],"block-image-html-large":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-600x400.jpg",600,400,true],"ct-gallery":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-330x220.jpg",330,220,true],"ct-section-header":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-1146x380.jpg",1146,380,true],"ct-thumb":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-86x57.jpg",86,57,true],"ct-thumb-large":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-167x111.jpg",167,111,true],"ct-small":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-280x187.jpg",280,187,true],"ct-medium":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-370x247.jpg",370,247,true],"ct-xmedium":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-960x640.jpg",960,640,true],"ct-large":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction.jpg",1280,853,false]},"uagb_author_info":{"display_name":"Dr. Samantha Kaeberlein, PharmD","author_link":"https:\/\/ameripharmaspecialty.com\/es\/author\/samantha\/"},"uagb_comment_info":0,"uagb_excerpt":"Lambert-Eaton syndrome (LEMS) is a rare disorder that occurs as a result of an immune system attack on the neuromuscular junction (a point where nerves send signals to your muscles). The damage at the neuromuscular junction causes impaired nerve signal transmission to the muscles, which results in gradual muscle weakness and a range of other&hellip;","rttpg_featured_image_url":{"full":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction.jpg",1280,853,false],"landscape":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction.jpg",1280,853,false],"portraits":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction.jpg",1280,853,false],"thumbnail":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-150x150.jpg",150,150,true],"medium":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-300x200.jpg",300,200,true],"large":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-1024x682.jpg",1024,682,true],"1536x1536":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction.jpg",1280,853,false],"2048x2048":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction.jpg",1280,853,false],"trp-custom-language-flag":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction.jpg",18,12,false],"block-image-html-large":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-600x400.jpg",600,400,true],"ct-gallery":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-330x220.jpg",330,220,true],"ct-section-header":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-1146x380.jpg",1146,380,true],"ct-thumb":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-86x57.jpg",86,57,true],"ct-thumb-large":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-167x111.jpg",167,111,true],"ct-small":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-280x187.jpg",280,187,true],"ct-medium":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-370x247.jpg",370,247,true],"ct-xmedium":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction-960x640.jpg",960,640,true],"ct-large":["https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2024\/02\/neuromuscular-junction.jpg",1280,853,false]},"rttpg_author":{"display_name":"Dr. Samantha Kaeberlein, PharmD","author_link":"https:\/\/ameripharmaspecialty.com\/es\/author\/samantha\/"},"rttpg_comment":0,"rttpg_category":"<a href=\"https:\/\/ameripharmaspecialty.com\/es\/category\/other-health-conditions\/\" rel=\"category tag\">Other Health Conditions<\/a>","rttpg_excerpt":"Lambert-Eaton syndrome (LEMS) is a rare disorder that occurs as a result of an immune system attack on the neuromuscular junction (a point where nerves send signals to your muscles). 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