{"id":21659,"date":"2022-10-05T10:12:22","date_gmt":"2022-10-05T17:12:22","guid":{"rendered":"https:\/\/ameripharmaspe.wpengine.com\/?p=21659"},"modified":"2026-03-20T15:32:17","modified_gmt":"2026-03-20T22:32:17","slug":"hemophagocytic-lymphohistiocytosis-hlh","status":"publish","type":"post","link":"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/","title":{"rendered":"Linfohistiocitosis hemofagoc\u00edtica (HLH)"},"content":{"rendered":"<p><span style=\"font-weight: 400;\">La linfohistiocitosis hemofagoc\u00edtica (LHH) es una enfermedad grave que puede ser mortal sin un diagn\u00f3stico temprano, tratamiento inmediato y cuidados intensivos. Se trata de un trastorno inmunitario poco frecuente que se caracteriza por una hiperactividad descontrolada de las c\u00e9lulas sangu\u00edneas asesinas, especialmente los linfocitos T (linfocitos T citot\u00f3xicos y linfocitos citol\u00edticos naturales) y los macr\u00f3fagos. Se caracteriza por una respuesta inflamatoria exagerada. Los fagocitos hiperactivados (linfocitos T citot\u00f3xicos) pueden atacar a otras c\u00e9lulas sangu\u00edneas y consumir los gl\u00f3bulos rojos (hemofogocitosis).<\/span><\/p>\n\n\n\n<div  id=\"call-to-action-736c90b4f8c73c55b53185e172a44bb9\" style=\"\" class=\"ct_call_to_action\">\n\t<div class=\"container\">\n\t\t<div class=\"block-wrap cta\">\n\t\t\t<div class=\"block-column\">\n\t\t\t\t<div class=\"cta_headings\">\n\t\t\t\t\t\t\t\t\t\t\t<h4 class=\"cta__heading\">\n\t\t\t\t\t\t\tObtenga asistencia para el copago\t\t\t\t\t\t<\/h4>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"cta__sub__heading\">\n\t\t\t\t\t\t\tHabla con un especialista\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\t<span class=\"cta_btn\">\n\t\t\t\t\t\t<a href=\"tel:8777780318\">(877) 778-0318<\/a>\n\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t<\/div>\n\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n\n<p><span style=\"font-weight: 400;\">La HLH es una enfermedad de progresi\u00f3n r\u00e1pida y potencialmente mortal que afecta principalmente a beb\u00e9s y j\u00f3venes, pero tambi\u00e9n puede presentarse en la poblaci\u00f3n de mayor edad.<\/span><\/p>\n\n\n\n<div id=\"ez-toc-container\" class=\"ez-toc-v2_0_82_2 counter-hierarchy ez-toc-counter ez-toc-custom ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Alternar tabla de contenido\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Palanca<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Types\" >Tipos<\/a><ul class='ez-toc-list-level-3' ><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Acquired_HLH\" >HLH adquirida<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Congenital_HLH_in_Babies\" >HLH cong\u00e9nita en beb\u00e9s<\/a><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Causes\" >Causas<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Difference_Between_Leukemia_and_HLH\" >Diferencia entre leucemia y HLH<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Signs_and_Symptoms\" >Signos y s\u00edntomas<\/a><ul class='ez-toc-list-level-3' ><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-7\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Fever\" >Fiebre<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-8\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Cytopenia\" >Citopenia<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-9\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Hepatosplenomegaly\" >Hepatoesplenomegalia<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-10\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Enlarged_Lymph_Nodes\" >Ganglios linf\u00e1ticos agrandados<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-11\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Jaundice\" >Ictericia<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-12\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Neurological_Dysfunction\" >Disfunci\u00f3n neurol\u00f3gica<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-13\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Renal_and_Cardiac_Problems\" >Problemas renales y card\u00edacos<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-14\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Hyperferritinemia\" >Hiperferritinemia<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-15\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Other_Symptoms\" >Otros s\u00edntomas<\/a><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-16\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Diagnosis\" >Diagn\u00f3stico<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-17\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Treatment\" >Tratamiento<\/a><ul class='ez-toc-list-level-3' ><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-18\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Medical_Treatment\" >Tratamiento m\u00e9dico<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-19\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Autologous_Stem_Cell_Transplant\" >Trasplante aut\u00f3logo de c\u00e9lulas madre&nbsp;<\/a><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-20\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Important_Points_To_Remember\" >Puntos importantes para recordar<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-21\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Survival_Rate\" >Tasa de supervivencia<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-22\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/#Ongoing_Research\" >Investigaci\u00f3n en curso<\/a><\/li><\/ul><\/nav><\/div>\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Types\"><\/span><span style=\"font-weight: 400;\">Tipos<\/span><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p><span style=\"font-weight: 400;\">La HLH se puede clasificar como cong\u00e9nita o adquirida.<\/span><\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Acquired_HLH\"><\/span><span style=\"font-weight: 400;\">HLH adquirida<\/span><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p><span style=\"font-weight: 400;\">La HLH adquirida puede presentarse en cualquier grupo de edad. La mayor\u00eda de los pacientes con HLH adquirida son personas inmunodeprimidas. La HLH adquirida se conoce a menudo como HLH secundaria porque suele ser secundaria a otras enfermedades, como:<\/span><\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li><span style=\"font-weight: 400;\">Infecci\u00f3n bacteriana, f\u00fangica o viral como la causada por el virus de Epstein-Barr o el citomegalovirus<\/span><\/li>\n\n\n\n<li><span style=\"font-weight: 400;\">Carcinomas como el linfoma de c\u00e9lulas T o <\/span><a href=\"https:\/\/www.sciencedirect.com\/topics\/medicine-and-dentistry\/prostate-adenocarcinoma\"><span style=\"font-weight: 400;\">adenocarcinoma de pr\u00f3stata<\/span><\/a><\/li>\n\n\n\n<li><span style=\"font-weight: 400;\">Neoplasias hematol\u00f3gicas (es decir, leucemia)<\/span><\/li>\n\n\n\n<li><span style=\"font-weight: 400;\">Enfermedades autoinmunes como las que atacan la m\u00e9dula \u00f3sea (es decir, enfermedades reumatol\u00f3gicas)<\/span><\/li>\n\n\n\n<li><span style=\"font-weight: 400;\">Enfermedades que se producen por la supresi\u00f3n del sistema inmunol\u00f3gico por el uso de medicamentos inmunosupresores, etc.<\/span><\/li>\n<\/ul>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Congenital_HLH_in_Babies\"><\/span><span style=\"font-weight: 400;\">HLH cong\u00e9nita en beb\u00e9s<\/span><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p><span style=\"font-weight: 400;\">La HLH cong\u00e9nita o familiar es un trastorno gen\u00e9tico que se hereda en los ni\u00f1os. La HLH familiar se presenta a una edad muy temprana, a menudo seguida de una infecci\u00f3n com\u00fan. El reci\u00e9n nacido presenta fiebre y un aumento de la actividad de las c\u00e9lulas T asesinas naturales, caracterizada por una respuesta hiperinflamatoria con signos de pancitopenia (disminuci\u00f3n del n\u00famero de los tres tipos de c\u00e9lulas sangu\u00edneas: gl\u00f3bulos rojos, gl\u00f3bulos blancos y plaquetas). Se presenta fiebre junto con hepatomegalia (agrandamiento del h\u00edgado) y esplenomegalia (agrandamiento del bazo). La HLH cong\u00e9nita tiene hasta cinco subtipos con mutaciones en diferentes genes relacionados con la regulaci\u00f3n de la producci\u00f3n y actividad de los fagocitos sangu\u00edneos. La HLH cong\u00e9nita tambi\u00e9n se conoce como &quot;linfohistiocitosis hemofagoc\u00edtica primaria&quot;.&nbsp;<\/span><\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Causes\"><\/span><span style=\"font-weight: 400;\">Causas<\/span><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p><span style=\"font-weight: 400;\">Se est\u00e1n realizando investigaciones para determinar la causa exacta de la HLH. Se cree que su causa es una etiolog\u00eda postinfecciosa a\u00fan por determinar. La etiolog\u00eda propuesta es que una infecci\u00f3n, una neoplasia maligna o el uso de f\u00e1rmacos quimioterap\u00e9uticos o inmunosupresores atacan el material gen\u00e9tico celular, especialmente en la m\u00e9dula \u00f3sea, principal sitio de producci\u00f3n de c\u00e9lulas sangu\u00edneas. Este da\u00f1o al ADN provoca la sobreproducci\u00f3n de ciertas c\u00e9lulas (p. ej., macr\u00f3fagos, linfocitos T citot\u00f3xicos y linfocitos T citol\u00edticos naturales). Estos fagocitos producen una respuesta hiperinflamatoria y atacan a otras c\u00e9lulas sangu\u00edneas del cuerpo (p. ej., gl\u00f3bulos rojos, plaquetas, granulocitos, etc.), lo que resulta en una condici\u00f3n pancitop\u00e9nica (supresi\u00f3n de las tres l\u00edneas celulares).<\/span><\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Difference_Between_Leukemia_and_HLH\"><\/span><span style=\"font-weight: 400;\">Diferencia entre leucemia y HLH<\/span><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p><span style=\"font-weight: 400;\">Las investigaciones muestran que existe un v\u00ednculo estrecho entre <\/span><a href=\"https:\/\/www.cancer.org\/cancer\/acute-myeloid-leukemia\/about\/what-is-aml.html\"><span style=\"font-weight: 400;\">leucemia mieloide<\/span><\/a><span style=\"font-weight: 400;\"> y enfermedad HLH. Las personas con leucemia pueden desarrollar HLH secundaria. La leucemia tambi\u00e9n se conoce como c\u00e1ncer de gl\u00f3bulos blancos. En esta afecci\u00f3n, se produce un aumento de la producci\u00f3n de gl\u00f3bulos blancos j\u00f3venes (GB) anormales que no pueden funcionar correctamente. Si bien la HLH produce m\u00e1s GB (especialmente macr\u00f3fagos y linfocitos T), estos no son c\u00e9lulas anormales, sino c\u00e9lulas asesinas hiperactivas que destruyen c\u00e9lulas malignas y diversos pat\u00f3genos. Debido a su hiperactividad, a menudo atacan a las c\u00e9lulas sangu\u00edneas sanas del propio cuerpo (que conforman la actividad general del sistema inmunitario), lo que provoca s\u00edntomas comunes de la leucemia.<\/span><\/p>\n\n\n\n<div  id=\"call-to-action-11f005eae21ec3ead017ceee2e28c809\" style=\"\" class=\"ct_call_to_action\">\n\t<div class=\"container\">\n\t\t<div class=\"block-wrap cta\">\n\t\t\t<div class=\"block-column\">\n\t\t\t\t<div class=\"cta_headings\">\n\t\t\t\t\t\t\t\t\t\t\t<h4 class=\"cta__heading\">\n\t\t\t\t\t\t\tConsulte con un especialista en quimioterapia\t\t\t\t\t\t<\/h4>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"cta__sub__heading\">\n\t\t\t\t\t\t\tObtenga asistencia para el tratamiento de quimioterapia\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\t<span class=\"cta_btn\">\n\t\t\t\t\t\t<a href=\"#form\">Programar una consulta<\/a>\n\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t<\/div>\n\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Signs_and_Symptoms\"><\/span><span style=\"font-weight: 400;\">Signos y s\u00edntomas<\/span><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p><span style=\"font-weight: 400;\">La HLH es un trastorno multisist\u00e9mico que afecta a numerosos \u00f3rganos, como la m\u00e9dula \u00f3sea, el h\u00edgado, el bazo, el cerebro, los ri\u00f1ones y el coraz\u00f3n, as\u00ed como a los tejidos corporales en general. Los signos y s\u00edntomas que puede presentar la HLH incluyen los siguientes:<\/span><\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Fever\"><\/span><span style=\"font-weight: 400;\">Fiebre<\/span><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"alignright\"><img loading=\"lazy\" decoding=\"async\" width=\"420\" height=\"280\" src=\"https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2022\/10\/nurse-taking-temperature.jpg\" alt=\"Nurse taking temperature\" class=\"wp-image-21665\" srcset=\"https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2022\/10\/nurse-taking-temperature.jpg 420w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2022\/10\/nurse-taking-temperature-300x200.jpg 300w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2022\/10\/nurse-taking-temperature-330x220.jpg 330w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2022\/10\/nurse-taking-temperature-86x57.jpg 86w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2022\/10\/nurse-taking-temperature-167x111.jpg 167w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2022\/10\/nurse-taking-temperature-280x187.jpg 280w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2022\/10\/nurse-taking-temperature-370x247.jpg 370w\" sizes=\"auto, (max-width: 420px) 100vw, 420px\" \/><\/figure>\n<\/div>\n\n\n<p><span style=\"font-weight: 400;\">Debido a la respuesta hiperinflamatoria de los gl\u00f3bulos blancos, hay una mayor cantidad de gl\u00f3bulos blancos circulantes. <\/span><a href=\"https:\/\/www.nature.com\/subjects\/lymphokines\"><span style=\"font-weight: 400;\">linfocinas<\/span><\/a><span style=\"font-weight: 400;\"> como las interleucinas y las bradicininas que controlan diversas funciones corporales como la regulaci\u00f3n de la temperatura corporal, lo que provoca fiebre y acumulaci\u00f3n de l\u00edquido en los tejidos.<\/span><\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Cytopenia\"><\/span><span style=\"font-weight: 400;\">Citopenia<\/span><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p><span style=\"font-weight: 400;\">Los fagocitos hiperactivados comienzan a atacar las c\u00e9lulas sangu\u00edneas que funcionan normalmente, lo que resulta en un bajo recuento de gl\u00f3bulos blancos que ayudan a prevenir infecciones. Por lo general, hay una disminuci\u00f3n en todos los tipos de c\u00e9lulas sangu\u00edneas, y esto puede afectar diferentes funciones corporales. Es importante que se realice an\u00e1lisis de sangre regularmente (es decir, hemograma completo, etc.). Los niveles bajos de gl\u00f3bulos rojos pueden causar dificultad para respirar debido a la disminuci\u00f3n del suministro de ox\u00edgeno a los tejidos. Puede experimentar fatiga, mareos, piel fr\u00eda, latidos card\u00edacos irregulares y piel p\u00e1lida y amarillenta. Si tiene s\u00edntomas de anemia, informe a su m\u00e9dico. Con la destrucci\u00f3n de gl\u00f3bulos rojos, gl\u00f3bulos blancos y plaquetas, el paciente corre el riesgo de anemia, dificultad para respirar y fatiga, pero m\u00e1s importante a\u00fan, el paciente corre el riesgo de infecciones bacterianas, f\u00fangicas y virales graves, y hemorragias graves.<\/span><\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Hepatosplenomegaly\"><\/span><span style=\"font-weight: 400;\">Hepatoesplenomegalia<\/span><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p><span style=\"font-weight: 400;\">Generalmente, la destrucci\u00f3n de c\u00e9lulas sangu\u00edneas ocurre en la m\u00e9dula \u00f3sea, el h\u00edgado, el bazo y los ganglios linf\u00e1ticos. Los fagocitos pueden acumularse en el bazo y el h\u00edgado, lo que provoca su agrandamiento. En casos graves, este agrandamiento puede hacerse visible en la superficie corporal, en la regi\u00f3n abdominal. Un h\u00edgado agrandado puede causar problemas relacionados con la disfunci\u00f3n hep\u00e1tica, como ictericia (que se explica m\u00e1s adelante), dolor abdominal y v\u00f3mitos.<\/span><\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Enlarged_Lymph_Nodes\"><\/span><span style=\"font-weight: 400;\">Ganglios linf\u00e1ticos agrandados<\/span><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p><span style=\"font-weight: 400;\">La acumulaci\u00f3n de fagocitos en los ganglios linf\u00e1ticos provoca su agrandamiento. Estos se inflaman y se puede sentir sensibilidad y dolor en la piel.<\/span><\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Jaundice\"><\/span><span style=\"font-weight: 400;\">Ictericia<\/span><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p><span style=\"font-weight: 400;\">La destrucci\u00f3n de gl\u00f3bulos rojos produce bilirrubina, el producto de degradaci\u00f3n de la hemoglobina. Esta bilirrubina se conjuga con sales como el glucuronato para hacerla m\u00e1s soluble y facilitar su excreci\u00f3n. En casos graves de destrucci\u00f3n de gl\u00f3bulos rojos, la producci\u00f3n de bilirrubina aumenta junto con la disminuci\u00f3n de la conjugaci\u00f3n debido a la disfunci\u00f3n hep\u00e1tica. La bilirrubina comienza a acumularse en la sangre, lo que provoca ictericia.<\/span><\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Neurological_Dysfunction\"><\/span><span style=\"font-weight: 400;\">Disfunci\u00f3n neurol\u00f3gica<\/span><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p><span style=\"font-weight: 400;\">Es posible que experimente s\u00edntomas neurol\u00f3gicos como: <\/span><a href=\"https:\/\/www.ninds.nih.gov\/health-information\/disorders\/encephalopathy\"><span style=\"font-weight: 400;\">encefalopat\u00eda<\/span><\/a><span style=\"font-weight: 400;\">La disfunci\u00f3n neurol\u00f3gica es secundaria a niveles elevados de bilirrubina, ferritina, triglic\u00e9ridos y otros productos de degradaci\u00f3n celular. Estos afectan el crecimiento y el desarrollo cerebral. La hipertrigliceridemia puede causar infarto cerebral secundario a problemas cardiovasculares.<\/span><\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Renal_and_Cardiac_Problems\"><\/span><span style=\"font-weight: 400;\">Problemas renales y card\u00edacos<\/span><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p><span style=\"font-weight: 400;\">Los niveles elevados de bilirrubina no conjugada a veces pueden causar insuficiencia renal grave. Destruye los t\u00fabulos renales\/nefronas al bloquearlos. La hipertrigliceridemia puede causar problemas cardiovasculares como... <\/span><a href=\"https:\/\/www.baptisthealth.com\/services\/heart-care\/conditions\/arteriosclerosis\"><span style=\"font-weight: 400;\">arteriosclerosis<\/span><\/a><span style=\"font-weight: 400;\">, aterosclerosis, bloqueo de la arteria coronaria e infarto de miocardio.<\/span><\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Hyperferritinemia\"><\/span><span style=\"font-weight: 400;\">Hiperferritinemia<\/span><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p><span style=\"font-weight: 400;\">La hiperferritinemia es un aumento de la concentraci\u00f3n plasm\u00e1tica de ferritina, una prote\u00edna transportadora de hierro. La destrucci\u00f3n de los gl\u00f3bulos rojos aumenta el contenido de hierro libre en la sangre. Este exceso de hierro se une a la ferritina y se convierte en su forma de almacenamiento. Un contenido elevado de hierro prolongado induce un aumento de la producci\u00f3n de ferritina, lo que causa hiperferritinemia.<\/span><\/p>\n\n\n\n<div  id=\"call-to-action-5f1fb81f3e00e6a48818c82b26d2c95b\" style=\"\" class=\"ct_call_to_action\">\n\t<div class=\"container\">\n\t\t<div class=\"block-wrap cta\">\n\t\t\t<div class=\"block-column\">\n\t\t\t\t<div class=\"cta_headings\">\n\t\t\t\t\t\t\t\t\t\t\t<h4 class=\"cta__heading\">\n\t\t\t\t\t\t\tInformaci\u00f3n sobre el tratamiento de la HLH\t\t\t\t\t\t<\/h4>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"cta__sub__heading\">\n\t\t\t\t\t\t\tObtener autorizaci\u00f3n previa\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\t<span class=\"cta_btn\">\n\t\t\t\t\t\t<a href=\"tel:8777780318\">(877) 778-0318<\/a>\n\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t<\/div>\n\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Other_Symptoms\"><\/span><span style=\"font-weight: 400;\">Otros s\u00edntomas<\/span><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p><span style=\"font-weight: 400;\">Pueden presentarse otros s\u00edntomas comunes de la enfermedad, como:<\/span><\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li><span style=\"font-weight: 400;\">Erupci\u00f3n cut\u00e1nea<\/span><\/li>\n\n\n\n<li><span style=\"font-weight: 400;\">N\u00e1useas<\/span><\/li>\n\n\n\n<li><span style=\"font-weight: 400;\">Dolor de cabeza<\/span><\/li>\n\n\n\n<li><span style=\"font-weight: 400;\">Trastornos respiratorios<\/span><\/li>\n\n\n\n<li><span style=\"font-weight: 400;\">P\u00e9rdida de peso<\/span><\/li>\n<\/ul>\n\n\n\n<p><span style=\"font-weight: 400;\">Curiosamente, existe un peque\u00f1o n\u00famero de casos de HLH en los que se han reportado tumores s\u00f3lidos. En algunos casos, los tumores se asociaron con HLH y se encontraron en c\u00e1ncer de mama, c\u00e1ncer de tiroides y adenocarcinoma de pr\u00f3stata.<\/span><\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Diagnosis\"><\/span><span style=\"font-weight: 400;\">Diagn\u00f3stico<\/span><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p><span style=\"font-weight: 400;\">El diagn\u00f3stico de la HLH es muy dif\u00edcil debido a su presentaci\u00f3n muy inespec\u00edfica. Debido a su rareza y naturaleza inespec\u00edfica, a menudo se produce un retraso en el diagn\u00f3stico. Con frecuencia, esta enfermedad se diagnostica err\u00f3neamente, lo que conlleva complicaciones adicionales e incluso la hace mortal.&nbsp;<\/span><\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">Seg\u00fan las investigaciones, la fiebre prolongada, los niveles elevados de ferritina en sangre y la disfunci\u00f3n hep\u00e1tica, <\/span><a href=\"https:\/\/www.cancer.gov\/publications\/dictionaries\/cancer-terms\/def\/cytopenia\"><span style=\"font-weight: 400;\">citopenias<\/span><\/a><span style=\"font-weight: 400;\">, y la hepatoesplenomegalia son las caracter\u00edsticas principales de la HLH que la hacen diferente de otros tipos de c\u00e1nceres de leucocitos.<\/span><\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">En pacientes con LHH tambi\u00e9n se observa coagulaci\u00f3n intravascular diseminada e inflamaci\u00f3n generalizada. Generalmente, no se presenta sepsis debido a la hiperactividad de los linfocitos.&nbsp;<\/span><\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">Una herramienta muy \u00fatil para diagnosticar la HLH es el hemograma. En algunos pacientes con HLH, al obtenerse un hemograma, se observ\u00f3 claramente que los macr\u00f3fagos hiperactivos estaban destruyendo los gl\u00f3bulos rojos del propio cuerpo (hemofogocitosis), una caracter\u00edstica importante de la enfermedad. Tambi\u00e9n se observ\u00f3 hiperfibrinogenemia en pacientes con HLH en algunos proyectos de investigaci\u00f3n.<\/span><\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Treatment\"><\/span><span style=\"font-weight: 400;\">Tratamiento<\/span><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p><span style=\"font-weight: 400;\">Dado que la HLH es un trastorno potencialmente mortal, el tratamiento debe iniciarse lo antes posible. Se deben administrar medicamentos de emergencia para prevenir la propagaci\u00f3n de la enfermedad y ayudar al cuerpo a recuperar sus funciones esenciales. Posteriormente, se determina la causa del trastorno subyacente y se administra la medicaci\u00f3n correspondiente.<\/span><\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">La terapia es de dos tipos principales: m\u00e9dica y quir\u00fargica.<\/span><\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Medical_Treatment\"><\/span><span style=\"font-weight: 400;\">Tratamiento m\u00e9dico<\/span><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p><span style=\"font-weight: 400;\">En primer lugar, se utilizan medicamentos para controlar y ralentizar la propagaci\u00f3n de la enfermedad. El control farmacol\u00f3gico consiste en diversos f\u00e1rmacos. Los corticosteroides, como la dexametasona, se utilizan para combatir la inflamaci\u00f3n. Los medicamentos inmunoterap\u00e9uticos se utilizan para fortalecer el sistema inmunitario del paciente. Si la LHH es secundaria a alguna infecci\u00f3n, como una infecci\u00f3n bacteriana, v\u00edrica o f\u00fangica, se utilizan los antibi\u00f3ticos correspondientes (p. ej., ciclosporina). Polivalente intravenoso. <\/span><a href=\"https:\/\/ameripharmaspecialty.com\/es\/ivig\/ivig\/\/immunoglobulins-ig\/\"><span style=\"font-weight: 400;\">inmunoglobulinas<\/span><\/a><span style=\"font-weight: 400;\"> Tambi\u00e9n se han utilizado en algunos ensayos.<\/span><\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">Luego vienen los productos qu\u00edmicos m\u00e1s t\u00f3xicos, como la quimioterapia. El etop\u00f3sido es uno de los principales medicamentos quimioterap\u00e9uticos que se administran a los pacientes con LHH. Otros medicamentos de quimioterapia incluyen <a href=\"https:\/\/ameripharmaspecialty.com\/es\/discontinued\/cyclophosphamide\/\">ciclofosfamida<\/a>, doxorrubicina, vincristina y prednisona.<\/span><\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">Cabe recordar que todos estos medicamentos se administran actualmente a modo de prueba. No existe un medicamento espec\u00edfico para curar la LHH. El trasplante de c\u00e9lulas madre o de m\u00e9dula \u00f3sea puede curar a algunos pacientes.&nbsp;<\/span><\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Autologous_Stem_Cell_Transplant\"><\/span><span style=\"font-weight: 400;\">Trasplante aut\u00f3logo de c\u00e9lulas madre&nbsp;<\/span><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p><a href=\"https:\/\/iscrm.uw.edu\/how-does-stem-cell-therapy-work\/\"><span style=\"font-weight: 400;\">Terapia con c\u00e9lulas madre<\/span><\/a><span style=\"font-weight: 400;\"> Se ha realizado en algunos casos, y los resultados obtenidos son alentadores. La terapia con c\u00e9lulas madre implica el uso de c\u00e9lulas madre sanas para tratar o prevenir enfermedades. En esta terapia, las c\u00e9lulas madre se extraen de una persona sana y se trasplantan a la m\u00e9dula \u00f3sea de la persona afectada.&nbsp;<\/span><\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">Antes de la terapia, se realizan una serie de pruebas diagn\u00f3sticas para garantizar la salud f\u00edsica del paciente y determinar si puede soportar el trasplante. Posteriormente, se le administra quimioterapia que destruye las c\u00e9lulas defectuosas de la m\u00e9dula \u00f3sea y se libera espacio para el trasplante de nuevas c\u00e9lulas. Este proceso se denomina &quot;acondicionamiento&quot;. Tras un acondicionamiento exitoso, se trasplantan c\u00e9lulas madre de un donante sano y compatible a la m\u00e9dula \u00f3sea del paciente. Posteriormente, el paciente recibe atenci\u00f3n m\u00e9dica constante.<\/span><\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">Una de las principales limitaciones de este tratamiento es el rechazo del trasplante. Las c\u00e9lulas inmunitarias del paciente pueden destruir las c\u00e9lulas reci\u00e9n trasplantadas. Otro problema importante es que este m\u00e9todo solo cura la forma familiar de LHH. Este m\u00e9todo no tiene la eficacia de 100%; en cambio, la tasa de trasplantes exitosos es tan baja como 40%.<\/span><\/p>\n\n\n\n<div  id=\"call-to-action-ddb6fca1d636f2bd2145a3eb9d9886c0\" style=\"\" class=\"ct_call_to_action\">\n\t<div class=\"container\">\n\t\t<div class=\"block-wrap cta\">\n\t\t\t<div class=\"block-column\">\n\t\t\t\t<div class=\"cta_headings\">\n\t\t\t\t\t\t\t\t\t\t\t<h4 class=\"cta__heading\">\n\t\t\t\t\t\t\tObtenga asistencia para el copago\t\t\t\t\t\t<\/h4>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"cta__sub__heading\">\n\t\t\t\t\t\t\tHabla con un especialista\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\t<span class=\"cta_btn\">\n\t\t\t\t\t\t<a href=\"#form\">Obtenga una evaluaci\u00f3n gratuita<\/a>\n\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t<\/div>\n\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Important_Points_To_Remember\"><\/span><span style=\"font-weight: 400;\">Puntos importantes para recordar<\/span><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p><span style=\"font-weight: 400;\">A continuaci\u00f3n se presentan algunos puntos importantes a recordar con respecto al tratamiento:<\/span><span style=\"font-weight: 400;\"><br><\/span><\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li><span style=\"font-weight: 400;\">Nunca se automedique.&nbsp;<\/span><\/li>\n\n\n\n<li><span style=\"font-weight: 400;\">Consulte siempre a su m\u00e9dico ante cualquier s\u00edntoma. Si nota cualquier aumento de volumen en la zona abdominal, el cuello, la ingle, los senos o la axila, busque atenci\u00f3n m\u00e9dica de inmediato. Realice pruebas de imagen como ecograf\u00eda, tomograf\u00eda computarizada o resonancia magn\u00e9tica si es necesario.&nbsp;<\/span><\/li>\n\n\n\n<li><span style=\"font-weight: 400;\">La dosis de un medicamento es espec\u00edfica para cada persona. Su m\u00e9dico puede aumentar o disminuir la dosis seg\u00fan la gravedad del c\u00e1ncer, la aparici\u00f3n de efectos adversos o la respuesta de su organismo al medicamento.<\/span><\/li>\n\n\n\n<li><span style=\"font-weight: 400;\">Debe seguir estrictamente las instrucciones de su m\u00e9dico. La dosis de un medicamento no debe ser mayor ni menor a la prescrita. Si omiti\u00f3 una dosis accidentalmente, no duplique la dosis. En su lugar, contin\u00fae con su pauta de dosificaci\u00f3n habitual o consulte a su m\u00e9dico si es necesario.<\/span><\/li>\n\n\n\n<li><span style=\"font-weight: 400;\">Si siente alguna molestia, no dude en informar a su m\u00e9dico. No oculte ning\u00fan s\u00edntoma. Inf\u00f3rmele adecuadamente para que pueda tomar las medidas necesarias.&nbsp;<\/span><\/li>\n\n\n\n<li><span style=\"font-weight: 400;\">Es posible que sienta n\u00e1useas y v\u00f3mitos agudos o retardados una vez que comience el tratamiento, ya que los medicamentos utilizados para tratar la HLH suelen ser quimioterap\u00e9uticos. Si un m\u00e9dico le receta un medicamento, preg\u00fantele sobre los efectos secundarios y obtenga pautas para evitar futuras emergencias. Los s\u00edntomas suelen desaparecer despu\u00e9s de unas horas o d\u00edas de comenzar la quimioterapia. De lo contrario, consulte a su m\u00e9dico. Cuide sus h\u00e1bitos alimenticios. Coma peque\u00f1as cantidades de cuatro a seis veces al d\u00eda y no coma demasiado de una sola vez. Mantenga una hidrataci\u00f3n corporal adecuada y tome l\u00edquidos a lo largo del d\u00eda.<\/span><\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Survival_Rate\"><\/span><span style=\"font-weight: 400;\">Tasa de supervivencia<\/span><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p><span style=\"font-weight: 400;\">Desafortunadamente, la tasa de supervivencia de la HLH es muy baja. Muchos casos tratados adecuadamente pueden tener una alta tasa de mortalidad. Esto se debe a m\u00faltiples factores (p. ej., diagn\u00f3stico tard\u00edo o incompleto, propagaci\u00f3n r\u00e1pida y progresiva de la enfermedad, falta de medicaci\u00f3n de eficacia comprobada, baja tasa de \u00e9xito de los trasplantes, etc.). Sin tratamiento, el paciente puede morir en cuesti\u00f3n de semanas o 1 <\/span><span style=\"font-weight: 400;\">\u2013 <\/span><span style=\"font-weight: 400;\">2 meses. Incluso con tratamiento y cuidados intensivos, una peque\u00f1a fracci\u00f3n de pacientes (20%) <\/span><span style=\"font-weight: 400;\">\u2013<\/span><span style=\"font-weight: 400;\"> 25%) tienen una esperanza de vida de 5 a\u00f1os.<\/span><\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">Actualmente, se ha dise\u00f1ado un nuevo protocolo farmacol\u00f3gico para tratar la HLH denominado \u201c<\/span><a href=\"https:\/\/ashpublications.org\/blood\/article\/100\/7\/2367\/106167\/Treatment-of-hemophagocytic-lymphohistiocytosis\"><span style=\"font-weight: 400;\">HLH-94<\/span><\/a><span style=\"font-weight: 400;\">Protocolo. Consiste en etop\u00f3sido junto con dexametasona. Esto ha dado como resultado una tasa de supervivencia global de 55% en algunos ensayos cl\u00ednicos.<\/span><\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">El pron\u00f3stico de la HLH var\u00eda en pacientes con HLH secundaria. Los pacientes con HLH secundaria a enfermedades autoinmunes tienen una mayor tasa de supervivencia que aquellos con HLH secundaria a tumores como el linfoma de c\u00e9lulas T.<\/span><\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Ongoing_Research\"><\/span><span style=\"font-weight: 400;\">Investigaci\u00f3n en curso<\/span><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p><span style=\"font-weight: 400;\">La investigaci\u00f3n actual se centra en determinar la causa exacta de la HLH. Se est\u00e1n realizando ensayos con diferentes protocolos m\u00e9dicos para encontrar un tratamiento espec\u00edfico. El uso de la terapia con c\u00e9lulas madre, la ingenier\u00eda gen\u00e9tica y la biotecnolog\u00eda para el tratamiento de este tipo de enfermedades es un \u00e1rea de investigaci\u00f3n activa.<\/span><\/p>","protected":false},"excerpt":{"rendered":"<p>La linfohistiocitosis hemofagoc\u00edtica (LHH) es una enfermedad grave que puede ser mortal sin un diagn\u00f3stico temprano, tratamiento inmediato y cuidados intensivos. Se trata de un trastorno inmunitario poco com\u00fan que se caracteriza por una hiperactividad descontrolada de las c\u00e9lulas hematopoy\u00e9ticas, especialmente las c\u00e9lulas T (c\u00e9lulas T citot\u00f3xicas y c\u00e9lulas asesinas naturales) y los macr\u00f3fagos.<\/p>","protected":false},"author":20,"featured_media":21661,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"om_disable_all_campaigns":false,"_uag_custom_page_level_css":"","footnotes":""},"categories":[4],"tags":[25],"class_list":["post-21659","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-other-health-conditions","tag-dr-haresh-jhangiani"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.5 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Hemophagocytic Lymphohistiocytosis (HLH) - AmeriPharma\u00ae Specialty Care<\/title>\n<meta name=\"description\" content=\"Learn about Hemophagocytic Lymphohistiocytosis (HLH) types, causes, signs and symptoms, diagnosis, and available treatment options.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/ameripharmaspecialty.com\/es\/other-health-conditions\/hemophagocytic-lymphohistiocytosis-hlh\/\" \/>\n<meta property=\"og:locale\" content=\"es_MX\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Hemophagocytic Lymphohistiocytosis (HLH) - 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