{"id":11997,"date":"2019-06-07T09:00:57","date_gmt":"2019-06-07T16:00:57","guid":{"rendered":"https:\/\/ameripharmaspe.wpengine.com\/?p=11997"},"modified":"2025-12-30T17:23:10","modified_gmt":"2025-12-31T00:23:10","slug":"classic-hemophilia-types-symptoms-treatment","status":"publish","type":"post","link":"https:\/\/ameripharmaspecialty.com\/es\/hemophilia\/classic-hemophilia-types-symptoms-treatment\/","title":{"rendered":"Hemofilia cl\u00e1sica: tipos, s\u00edntomas y tratamiento"},"content":{"rendered":"<p><span style=\"font-weight: 400;\">La coagulaci\u00f3n es necesaria para detener el sangrado y es esencial para la cicatrizaci\u00f3n de heridas. Sin embargo, aquellos con<\/span><a href=\"https:\/\/ameripharmaspecialty.com\/es\/conditions-treatments\/hemophilia\/\"> <span style=\"font-weight: 400;\">hemofilia<\/span><\/a><span style=\"font-weight: 400;\"> no son capaces de producir los niveles necesarios de ciertos factores de coagulaci\u00f3n y, por tanto, experimentan consecuencias para la salud.<\/span><\/p>\n\n\n\n<blockquote class=\"wp-block-quote is-layout-flow wp-block-quote-is-layout-flow\">\n<p><span style=\"font-weight: 400;\">La hemofilia es un trastorno gen\u00e9tico poco com\u00fan en el que la sangre de una persona tiene dificultades para coagularse, lo que provoca dolor y graves problemas de salud.<\/span><\/p>\n<\/blockquote>\n\n\n\n<div  id=\"call-to-action-aa573cf18ee7cfb24e12cd65ac69553a\" style=\"\" class=\"ct_call_to_action\">\n\t<div class=\"container\">\n\t\t<div class=\"block-wrap cta\">\n\t\t\t<div class=\"block-column\">\n\t\t\t\t<div class=\"cta_headings\">\n\t\t\t\t\t\t\t\t\t\t\t<h4 class=\"cta__heading\">\n\t\t\t\t\t\t\t\u00bfPuede ayudar la IgIV?\t\t\t\t\t\t<\/h4>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"cta__sub__heading\">\n\t\t\t\t\t\t\tInformaci\u00f3n gratuita sobre el tratamiento con IgIV | \u00bfDificultad para diagnosticar?\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\t<span class=\"cta_btn\">\n\t\t\t\t\t\t<a href=\"#form\">Consulte a un especialista en IgIV<\/a>\n\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t<\/div>\n\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n\n<div id=\"ez-toc-container\" class=\"ez-toc-v2_0_83 counter-hierarchy ez-toc-counter ez-toc-custom ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Alternar tabla de contenido\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Palanca<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/ameripharmaspecialty.com\/es\/hemophilia\/classic-hemophilia-types-symptoms-treatment\/#Types_of_Hemophilia\" >Tipos de hemofilia<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/ameripharmaspecialty.com\/es\/hemophilia\/classic-hemophilia-types-symptoms-treatment\/#What_Are_the_Symptoms\" >\u00bfCu\u00e1les son los s\u00edntomas?<\/a><ul class='ez-toc-list-level-3' ><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/ameripharmaspecialty.com\/es\/hemophilia\/classic-hemophilia-types-symptoms-treatment\/#Mild_Hemophilia\" >Hemofilia leve<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/ameripharmaspecialty.com\/es\/hemophilia\/classic-hemophilia-types-symptoms-treatment\/#Moderate_Hemophilia\" >Hemofilia moderada<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/ameripharmaspecialty.com\/es\/hemophilia\/classic-hemophilia-types-symptoms-treatment\/#Severe_Hemophilia\" >Hemofilia grave<\/a><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/ameripharmaspecialty.com\/es\/hemophilia\/classic-hemophilia-types-symptoms-treatment\/#Whos_at_Risk_and_How_To_Get_Tested\" >\u00bfQui\u00e9n est\u00e1 en riesgo y c\u00f3mo hacerse la prueba?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-7\" href=\"https:\/\/ameripharmaspecialty.com\/es\/hemophilia\/classic-hemophilia-types-symptoms-treatment\/#Hemophilia_Treatment_Options\" >Opciones de tratamiento para la hemofilia<\/a><ul class='ez-toc-list-level-3' ><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-8\" href=\"https:\/\/ameripharmaspecialty.com\/es\/hemophilia\/classic-hemophilia-types-symptoms-treatment\/#Pain_Management\" >Manejo del dolor<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-9\" href=\"https:\/\/ameripharmaspecialty.com\/es\/hemophilia\/classic-hemophilia-types-symptoms-treatment\/#Inhibitors_When_the_Body_Rejects_Treatment\" >Inhibidores: Cuando el cuerpo rechaza el tratamiento<\/a><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-10\" href=\"https:\/\/ameripharmaspecialty.com\/es\/hemophilia\/classic-hemophilia-types-symptoms-treatment\/#Conclusion\" >Conclusi\u00f3n<\/a><\/li><\/ul><\/nav><\/div>\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Types_of_Hemophilia\"><\/span>Tipos de hemofilia<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p><span style=\"font-weight: 400;\">Seg\u00fan el <a href=\"https:\/\/www.cdc.gov\/hemophilia\/about\/index.html\">Centro para el Control y la Prevenci\u00f3n de Enfermedades<\/a>Las dos formas m\u00e1s comunes de esta enfermedad son:<\/span><\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li><span style=\"font-weight: 400;\">Hemofilia A (hemofilia cl\u00e1sica) en la que una persona tiene niveles insuficientes de factor de coagulaci\u00f3n VIII (8)<\/span><\/li>\n\n\n\n<li><span style=\"font-weight: 400;\">Hemofilia B (enfermedad de Christmas) causada por niveles bajos del factor de coagulaci\u00f3n IX (9).<\/span><\/li>\n<\/ul>\n\n\n\n<p><span style=\"font-weight: 400;\">Este \u00faltimo es menos com\u00fan, pero ambas afecciones tienen los mismos s\u00edntomas.<\/span><\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"What_Are_the_Symptoms\"><\/span>\u00bfCu\u00e1les son los s\u00edntomas?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Los s\u00edntomas de la hemofilia dependen en gran medida de qu\u00e9 tan bajos sean los niveles de factores de coagulaci\u00f3n: leves, moderados o graves.<\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Mild_Hemophilia\"><\/span><strong>Hemofilia leve<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Las personas con hemofilia leve pueden no sangrar con m\u00e1s frecuencia de lo habitual en su vida diaria, pero pueden experimentar sangrados m\u00e1s prolongados de lo normal despu\u00e9s de una cirug\u00eda, un tratamiento dental, lesiones o cortes profundos. Tambi\u00e9n pueden aparecer hematomas con mayor facilidad que en personas sin hemofilia.<\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Moderate_Hemophilia\"><\/span><strong>Hemofilia moderada<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Las personas con hemofilia moderada pueden experimentar sangrado despu\u00e9s de lesiones menores, cirug\u00edas o procedimientos dentales, y en ocasiones pueden presentar episodios de sangrado espont\u00e1neo, especialmente en articulaciones y m\u00fasculos. Estos sangrados pueden no ser tan frecuentes como en la hemofilia grave, pero aun as\u00ed requieren tratamiento inmediato.<\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Severe_Hemophilia\"><\/span><strong>Hemofilia grave<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Una persona con hemofilia grave tiene mayor probabilidad de sufrir hemorragias internas espont\u00e1neas, especialmente en las articulaciones y los m\u00fasculos. Estas hemorragias pueden causar hinchaz\u00f3n, calor, hematomas y dolor intenso, y con el tiempo pueden provocar da\u00f1o articular cr\u00f3nico si no se tratan r\u00e1pidamente. Las personas con hemofilia tambi\u00e9n pueden experimentar hemorragias nasales frecuentes, sangrado prolongado por cortes y, en ocasiones, sangre en la orina o las heces.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Whos_at_Risk_and_How_To_Get_Tested\"><\/span>\u00bfQui\u00e9n est\u00e1 en riesgo y c\u00f3mo hacerse la prueba?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<h2 class=\"wp-block-heading\"><strong><img loading=\"lazy\" decoding=\"async\" class=\"size-full wp-image-12290 alignright\" src=\"https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2019\/06\/hemophilia-lab-small.jpg\" alt=\"\" width=\"400\" height=\"266\" srcset=\"https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2019\/06\/hemophilia-lab-small.jpg 400w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2019\/06\/hemophilia-lab-small-300x200.jpg 300w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2019\/06\/hemophilia-lab-small-330x220.jpg 330w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2019\/06\/hemophilia-lab-small-86x57.jpg 86w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2019\/06\/hemophilia-lab-small-167x111.jpg 167w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2019\/06\/hemophilia-lab-small-280x186.jpg 280w, https:\/\/ameripharmaspecialty.com\/wp-content\/uploads\/2019\/06\/hemophilia-lab-small-370x246.jpg 370w\" sizes=\"auto, (max-width: 400px) 100vw, 400px\" \/><\/strong><\/h2>\n\n\n\n<p>La hemofilia suele estar causada por un cambio (mutaci\u00f3n) en un gen que proporciona instrucciones para la producci\u00f3n de factor de coagulaci\u00f3n. Generalmente se hereda y est\u00e1 presente al nacer. Dado que el gen se encuentra en el cromosoma X, la hemofilia es m\u00e1s com\u00fan en varones. Las mujeres portadoras del gen pueden ser &quot;portadoras&quot;, pero muchas tambi\u00e9n presentan niveles bajos de factor de coagulaci\u00f3n y pueden experimentar s\u00edntomas similares a los de la hemofilia leve, como sangrado menstrual abundante o propensi\u00f3n a la formaci\u00f3n de hematomas.<\/p>\n\n\n\n<p>Si tiene antecedentes familiares de hemofilia, incluyendo mujeres portadoras, es importante consultar con su m\u00e9dico sobre las pruebas. La hemofilia se diagnostica mediante an\u00e1lisis de sangre que miden los niveles de factores de coagulaci\u00f3n y la funci\u00f3n de coagulaci\u00f3n general. En algunos casos, se pueden recomendar pruebas gen\u00e9ticas para confirmar el diagn\u00f3stico o identificar portadores en la familia.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Hemophilia_Treatment_Options\"><\/span>Opciones de tratamiento para la hemofilia<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p><span style=\"font-weight: 400;\">Despu\u00e9s de ser diagnosticado con hemofilia, es importante comenzar el tratamiento adecuado lo antes posible.<\/span><\/p>\n\n\n\n<div  id=\"call-to-action-2f88e1ba6ec71c85deb5eb0f8f9c529c\" style=\"\" class=\"ct_call_to_action\">\n\t<div class=\"container\">\n\t\t<div class=\"block-wrap cta\">\n\t\t\t<div class=\"block-column\">\n\t\t\t\t<div class=\"cta_headings\">\n\t\t\t\t\t\t\t\t\t\t\t<h4 class=\"cta__heading\">\n\t\t\t\t\t\t\tObtenga asistencia para el copago de IgIV\t\t\t\t\t\t<\/h4>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"cta__sub__heading\">\n\t\t\t\t\t\t\tInformaci\u00f3n sobre su tratamiento con IgIV | Obtenga autorizaci\u00f3n previa para IgIV\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\t<span class=\"cta_btn\">\n\t\t\t\t\t\t<a href=\"#form\">Consulte a un especialista en IgIV<\/a>\n\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t<\/div>\n\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>Tratamiento a demanda:<\/strong> Las personas con hemofilia leve podr\u00edan necesitar tratamiento solo cuando se produce una hemorragia. Este suele consistir en la infusi\u00f3n del factor de coagulaci\u00f3n faltante para detener la hemorragia activa y prevenir complicaciones.<\/li>\n<\/ul>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>Tratamiento profil\u00e1ctico (preventivo):<\/strong> Las personas con hemofilia moderada a grave suelen recibir tratamiento profil\u00e1ctico regular, que consiste en la infusi\u00f3n de factor de coagulaci\u00f3n seg\u00fan un programa (por ejemplo, varias veces por semana) para mantener los niveles lo suficientemente altos como para reducir o prevenir las hemorragias espont\u00e1neas. Este enfoque ayuda a proteger las articulaciones y mejora la calidad de vida a largo plazo.<\/li>\n<\/ul>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Pain_Management\"><\/span><strong>Manejo del dolor<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Es posible que se necesiten analg\u00e9sicos para aliviar las molestias causadas por hemorragias articulares o musculares. Sin embargo, algunos medicamentos, como la aspirina y muchos otros... <a href=\"https:\/\/my.clevelandclinic.org\/health\/treatments\/11086-non-steroidal-anti-inflammatory-medicines-nsaids\">medicamentos antiinflamatorios no esteroides<\/a> (AINE) \u2014pueden afectar la funci\u00f3n plaquetaria y aumentar el riesgo de sangrado. Los pacientes solo deben usar analg\u00e9sicos considerados seguros para personas con trastornos hemorr\u00e1gicos y siempre deben consultar a su m\u00e9dico o centro de tratamiento de hemofilia antes de tomar cualquier medicamento nuevo.<\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Inhibitors_When_the_Body_Rejects_Treatment\"><\/span><strong>Inhibidores: Cuando el cuerpo rechaza el tratamiento<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Aproximadamente entre el 15% y el 20% de las personas con hemofilia A y un porcentaje menor con hemofilia B desarrollan <strong>inhibidores<\/strong>\u2014anticuerpos que el sistema inmunitario forma contra el factor de coagulaci\u00f3n infundido. Estos inhibidores impiden que el tratamiento sea eficaz porque el cuerpo &quot;rechaza&quot; el factor suplementario. Cuando se desarrollan inhibidores, los pacientes suelen necesitar tratamientos alternativos o especializados, que pueden ser m\u00e1s complejos y costosos. La monitorizaci\u00f3n estrecha por parte de un hemat\u00f3logo o un centro de tratamiento de hemofilia es esencial para controlar los inhibidores y ajustar la terapia.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Conclusion\"><\/span>Conclusi\u00f3n<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>En los \u00faltimos a\u00f1os, el tratamiento para la hemofilia se ha vuelto mucho m\u00e1s eficaz, lo que permite a muchas personas con esta afecci\u00f3n llevar una vida sana, activa y productiva. La clave es buscar tratamiento temprano, seguir un plan de atenci\u00f3n personalizado y colaborar estrechamente con especialistas para controlar los s\u00edntomas y prevenir complicaciones. Consulte con su m\u00e9dico sobre la posibilidad de colaborar con... <strong><a href=\"#form\">Cuidado especializado AmeriPharma\u00ae<\/a><\/strong> Para ayudarle a controlar la hemofilia. Nuestros farmac\u00e9uticos dedicados est\u00e1n disponibles las 24 horas, los 7 d\u00edas de la semana, los 365 d\u00edas del a\u00f1o para responder a sus preguntas, coordinar su medicaci\u00f3n y apoyarle durante todo su tratamiento.<\/p>","protected":false},"excerpt":{"rendered":"<p>La coagulaci\u00f3n es necesaria para detener el sangrado y es esencial para la cicatrizaci\u00f3n de heridas. Sin embargo, las personas con hemofilia no pueden producir los niveles necesarios de ciertos factores de coagulaci\u00f3n y, por lo tanto, sufren consecuencias para la salud.<\/p>","protected":false},"author":25,"featured_media":12287,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"om_disable_all_campaigns":false,"_uag_custom_page_level_css":"","footnotes":""},"categories":[6],"tags":[31],"class_list":["post-11997","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-hemophilia","tag-dr-mark-alfonso"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.5 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Classic Hemophilia: Types, Symptoms &amp; Treatment<\/title>\n<meta name=\"description\" content=\"Hemophilia is a rare disorder that prevents or delays blood clotting. Learn more about hemophilia and how to get tested and treated.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/ameripharmaspecialty.com\/es\/hemophilia\/classic-hemophilia-types-symptoms-treatment\/\" \/>\n<meta property=\"og:locale\" content=\"es_MX\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Classic Hemophilia: Types, Symptoms &amp; Treatment\" \/>\n<meta property=\"og:description\" content=\"Hemophilia is a rare disorder that prevents or delays blood clotting. 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